Wild-type ATTR amyloidosis generally has a better prognosis compared to hereditary ATTR amyloidosis (hATTR). Here are the key points:
- Wild-type ATTR amyloidosis
- Typically diagnosed in people aged 65 or older.
- Develops slowly over time as amyloid deposits form.
- Prognosis is generally better than for AL Show Full Answer
Wild-type ATTR amyloidosis generally has a better prognosis compared to hereditary ATTR amyloidosis (hATTR). Here are the key points:
- Wild-type ATTR amyloidosis:
- Typically diagnosed in people aged 65 or older.
- Develops slowly over time as amyloid deposits form.
- Prognosis is generally better than for AL amyloidosis or hATTR amyloidosis.
- Hereditary ATTR amyloidosis (hATTR):
- Life expectancy is about 4.7 years after diagnosis for half of the people.
- New treatments are extending life expectancy by stabilizing TTR proteins or stopping their production.
In summary, wild-type ATTR amyloidosis tends to have a better life expectancy compared to hereditary ATTR amyloidosis.
September 15, 2024